About The Medical Condition Angiomatosis, Meningo-Oculo-Facial

ClusterMed

Find the definition of the medical term Angiomatosis, Meningo-Oculo-Facial. Angiomatosis, Meningo-Oculo-Facial defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Angiomatosis, Meningo-Oculo-Facial

Angiomatosis, Meningo-Oculo-Facial Medical Condition Defined & Explained
Angiomatosis, Meningo-Oculo-Facial Medical Condition

What's The Definition Of The Medical Condition Angiomatosis, Meningo-Oculo-Facial?

A congenital syndrome characterized by a port-wine nevus covering portions of the face and cranium (in the distribution of the ophthalmic division of the TRIGEMINAL NERVE) and angiomas of the meninges and choroid. Clinical manifestations include the onset of focal SEIZURES, progressive hemiparesis, GLAUCOMA, hemianopsia, and cognitive deficits in the first decade of life. By age two years, skull radiographs reveal "tramline calcifications" of the margins of the occipital and parietal lobes. Pathologically cortical neurons are replaced by glial tissue that undergoes calcification. (From Adams et al., Principles of Neurology, 6th ed, pp1018-9)

More Medical Conditions

A | B | C | D | E | F | G | H | I | J | K | L | M | N | O | P | Q | R | S | T | U | V | W | X | Y | Z

Medical Conditions Definitions Of The Day