About The Medical Condition Atrophy, Pigmentary Pallidal

ClusterMed

Find the definition of the medical term Atrophy, Pigmentary Pallidal. Atrophy, Pigmentary Pallidal defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Atrophy, Pigmentary Pallidal

Atrophy, Pigmentary Pallidal Medical Condition Defined & Explained
Atrophy, Pigmentary Pallidal Medical Condition

What's The Definition Of The Medical Condition Atrophy, Pigmentary Pallidal?

A rare autosomal recessive degenerative disorder which usually presents in late childhood or adolescence. Clinical manifestations include progressive MUSCLE SPASTICITY; hyperreflexia; MUSCLE RIGIDITY; DYSTONIA; DYSARTHRIA; and intellectual deterioration which progresses to severe dementia over several years. Pathologic examination reveals neuronal atrophy in the globus pallidus and iron deposition in blood vessels and perivascular spaces. (From Adams et al., Principles of Neurology, 6th ed, p972; Davis & Robertson, Textbook of Neuropathology, 2nd ed, pp972-929)

More Medical Conditions

A | B | C | D | E | F | G | H | I | J | K | L | M | N | O | P | Q | R | S | T | U | V | W | X | Y | Z

Medical Conditions Definitions Of The Day