About The Medical Condition Glycogen Debranching Enzyme System

ClusterMed

Find the definition of the medical term Glycogen Debranching Enzyme System. Glycogen Debranching Enzyme System defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Glycogen Debranching Enzyme System

Glycogen Debranching Enzyme System Medical Condition Defined & Explained
Glycogen Debranching Enzyme System Medical Condition

What's The Definition Of The Medical Condition Glycogen Debranching Enzyme System?

1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.

More Medical Conditions

A | B | C | D | E | F | G | H | I | J | K | L | M | N | O | P | Q | R | S | T | U | V | W | X | Y | Z

Medical Conditions Definitions Of The Day