About The Medical Condition Inherited Spongiform Encephalopathy, Gerstmann-Straussler
Find the definition of the medical term Inherited Spongiform Encephalopathy, Gerstmann-Straussler. Inherited Spongiform Encephalopathy, Gerstmann-Straussler defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.
Inherited Spongiform Encephalopathy, Gerstmann-Straussler
| Inherited Spongiform Encephalopathy, Gerstmann-Straussler Medical Condition |
|---|
What's The Definition Of The Medical Condition Inherited Spongiform Encephalopathy, Gerstmann-Straussler?
An autosomal dominant familial prion disease with a wide spectrum of clinical presentations including ATAXIA, spastic paraparesis, extrapyramidal signs, and DEMENTIA. Clinical onset is in the third to sixth decade of life and the mean duration of illness prior to death is five years. Several kindreds with variable clinical and pathologic features have been described. Pathologic features include cerebral prion protein amyloidosis, and spongiform or neurofibrillary degeneration. (From Brain Pathol 1998 Jul;8(3):499-513; Brain Pathol 1995 Jan;5(1):61-75)
|
More Medical Conditions
A | B | C | D | E | F | G | H | I | J | K | L | M | N | O | P | Q | R | S | T | U | V | W | X | Y | Z
Medical Conditions Definitions Of The Day
- Respiratory System Diagnostic Technics ‐ Methods and procedures for the diagnosis of diseases of the respiratory…
- Klofelin ‐ An alpha-2 adrenergic agonist that crosses the blood-brain barrier.…
- Pregnancy in Adolescence ‐ Pregnancy in humans…
- Chlortetracycline Hydrochloride ‐ An antibiotic substance isolated from the substrate of Streptomyces…
- Methylmesilate ‐ An alkylating agent in cancer therapy that may also act as a…
- Oscillometry ‐ Measurement of oscillations of any kind. In medicine it is used…
- Marriage Therapies ‐ A form of psychotherapy involving the husband and wife and directed…
- Fetal Tissue Donations ‐ Transference of fetal tissue between individuals of the same…
- Clot Retraction ‐ Retraction of a clot resulting from contraction of platelet pseudopods…
- Composition, Body ‐ The relative amounts of various components in the body, such…