About The Medical Condition Meningo-Oculo-Facial Angiomatosis

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Find the definition of the medical term Meningo-Oculo-Facial Angiomatosis. Meningo-Oculo-Facial Angiomatosis defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Meningo-Oculo-Facial Angiomatosis

Meningo-Oculo-Facial Angiomatosis Medical Condition Defined & Explained
Meningo-Oculo-Facial Angiomatosis Medical Condition

What's The Definition Of The Medical Condition Meningo-Oculo-Facial Angiomatosis?

A congenital syndrome characterized by a port-wine nevus covering portions of the face and cranium (in the distribution of the ophthalmic division of the TRIGEMINAL NERVE) and angiomas of the meninges and choroid. Clinical manifestations include the onset of focal SEIZURES, progressive hemiparesis, GLAUCOMA, hemianopsia, and cognitive deficits in the first decade of life. By age two years, skull radiographs reveal "tramline calcifications" of the margins of the occipital and parietal lobes. Pathologically cortical neurons are replaced by glial tissue that undergoes calcification. (From Adams et al., Principles of Neurology, 6th ed, pp1018-9)

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