About The Medical Condition Pigmentary Pallidal Atrophies

ClusterMed

Find the definition of the medical term Pigmentary Pallidal Atrophies. Pigmentary Pallidal Atrophies defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Pigmentary Pallidal Atrophies

Pigmentary Pallidal Atrophies Medical Condition Defined & Explained
Pigmentary Pallidal Atrophies Medical Condition

What's The Definition Of The Medical Condition Pigmentary Pallidal Atrophies?

A rare autosomal recessive degenerative disorder which usually presents in late childhood or adolescence. Clinical manifestations include progressive MUSCLE SPASTICITY; hyperreflexia; MUSCLE RIGIDITY; DYSTONIA; DYSARTHRIA; and intellectual deterioration which progresses to severe dementia over several years. Pathologic examination reveals neuronal atrophy in the globus pallidus and iron deposition in blood vessels and perivascular spaces. (From Adams et al., Principles of Neurology, 6th ed, p972; Davis & Robertson, Textbook of Neuropathology, 2nd ed, pp972-929)

More Medical Conditions

A | B | C | D | E | F | G | H | I | J | K | L | M | N | O | P | Q | R | S | T | U | V | W | X | Y | Z

Medical Conditions Definitions Of The Day