About The Medical Condition Ramsay Hunt Dentate Syndrome

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Find the definition of the medical term Ramsay Hunt Dentate Syndrome. Ramsay Hunt Dentate Syndrome defined and explained for easy understanding at the Medical Conditions from ClusterMed.info.

Ramsay Hunt Dentate Syndrome

Ramsay Hunt Dentate Syndrome Medical Condition Defined & Explained
Ramsay Hunt Dentate Syndrome Medical Condition

What's The Definition Of The Medical Condition Ramsay Hunt Dentate Syndrome?

A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)

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